Some forms of maple syrup urine disease are amenable to treatment with large doses of dietary thiamine.

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Some forms of maple syrup urine disease are amenable to treatment with large doses of dietary thiamine. What metabolic defect is being treated in these cases?

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Fundamentals of biochemistry Life at the Molecular Level

ISBN: 978-0470547847

4th edition

Authors: Donald Voet, Judith G. Voet, Charlotte W. Pratt

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Question Posted: Apr 30, 2016 02:50 PM

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Some forms of maple syrup urine disease are amenable to treatment with large doses of dietary thiamine.

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In such cases the defect is poor binding of thiamine pyrophos...View the full answer

Fundamentals of biochemistry Life at the Molecular Level

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